Concentration Details

Metabolite
HMDB0000489 (Aspartylglycosamine)
Biospecimen
Urine
Status
Detected and Quantified
Data source
Referenced
Concentration
70.383 (30.420-97.621) umol/mmol creatinine
Age
Children (1-13 years old)
Sex
Both
Condition
Aspartylglucosaminuria
References
    1. Aula P, Raivio KO, Maury P: Variation of urinary excretion of aspartylglucosamine and associated clinical findings in aspartyglucosaminuria. J Inherit Metab Dis. 1980;3(4):159-62. [PubMed:6787338 ]